Congenital orbital teratoma
نویسندگان
چکیده
BACKGROUND The occurrence of proptosis at birth is unusual and may be associated with a variety of tumours and structural abnormalities. Congenital orbital teratoma is a rare cause of congenital proptosis. METHODS A case report is presented of a female infant with gross right proptosis. RESULTS Computed tomography demonstrated a characteristic multicystic structure with no intracranial involvement. Histological examination found tissues derived from all three germ cell layers, consistent with a congenita orbital teratoma. The tumour was successfully removed preserving the globe and vision. CONCLUSIONS This report is an example of how early surgical intervention may allow preservation of the globe and vision in some patients with congenital orbital teratoma.
منابع مشابه
Congenital orbital-intracranial teratoma with subsequent malignancy: case report.
A newborn baby had an orbital-intracranial benign teratoma radically excised with preservation of the eye. Three years later she developed recurrent proptosis, and reoperation showed an invasive orbital tumour that histologically was a malignant germ-cell neoplasm. The relationship of the two tumours is discussed. Malignant change in a benign orbital-intracranial teratoma of the newborn has not...
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